Sclerosing epithelioid fibrosarcoma: rare and serious

Sclerosing Epithelioid Fibrosarcoma (SEF) is a rare form of soft tissue sarcoma. It is characterized by a slow evolution, with local recurrences and late metastases that are mainly pulmonary and pleural in about 50% of cases. The treatment is based on the surgery which must be as wide as possible. T...

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Bibliographic Details
Published in:The Pan African medical journal 2020-06, Vol.36 (131), p.131
Main Authors: Yahyaoui, Mounir, Benhammou, Mohammed, Aharram, Soufiane, Amghar, Jawad, Sadougui, Mohammed, Agoumi, Omar, Daoudi, Abdelkrim
Format: Article
Language:English
Subjects:
adjuvant treatment
Case Report
Chemotherapy, Adjuvant
Combined Modality Therapy
Female
Fibrosarcoma - diagnosis
Fibrosarcoma - pathology
Fibrosarcoma - surgery
Follow-Up Studies
Humans
metastases
Neoplasm Recurrence, Local
Radiotherapy, Adjuvant
recurrences
sclerosing epithelioid fibrosarcoma
surgery
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Description
Summary:Sclerosing Epithelioid Fibrosarcoma (SEF) is a rare form of soft tissue sarcoma. It is characterized by a slow evolution, with local recurrences and late metastases that are mainly pulmonary and pleural in about 50% of cases. The treatment is based on the surgery which must be as wide as possible. The efficacy of adjuvant therapy in the control of SEF is not yet demonstrated. Chemotherapy is used in recurrences, some have also proposed radiotherapy. Long-term follow-up of patients with SEF is therefore essential.
ISSN:1937-8688
1937-8688
DOI:10.11604/pamj.2020.36.131.18668