Subgaleal and epidural metastases of the undifferentiated embryonal sarcoma of the liver

Undifferentiated embryonal sarcoma of the liver (UESL) is very rare and has a very poor prognosis. UESL metastases have been reported in 5%-13% of the children with UESL and most metastases reported in the literature are present at diagnosis. Metastases reported in the literature belong to the lungs...

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Bibliographic Details
Published in:Radiology case reports 2022-01, Vol.17 (1), p.147-151
Main Authors: Dogan, Gulec Mert, Sığırcı, Ahmet, Okut, Gokalp, Dogan, Sait Murat, Yilmaz, Sezai
Format: Article
Language:English
Subjects:
Case Report
Epidural
Liver
Magnetic resonance image
Metastasis
Pediatric
Sarcoma
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Summary:Undifferentiated embryonal sarcoma of the liver (UESL) is very rare and has a very poor prognosis. UESL metastases have been reported in 5%-13% of the children with UESL and most metastases reported in the literature are present at diagnosis. Metastases reported in the literature belong to the lungs, pleura, and peritoneum. Radiological diagnosis of the UESL remains a poorly understood problem due to its rarity. Most of the reports published in the literature are also based on a relatively small number of patients. Approximately 200 cases have been reported regarding imaging features of this tumor. We reported a girl with UESL, who applied to the emergency department with abdominal pain. The lesion was solid and had cystic areas on ultrasound and there were peripherally enhanced serpenginous vessels in the lesion on Computed Tomography and MRI. Immunohistochemical diagnosis of the lesion was UESL. 26 months after surgery and adjuvant chemotherapy extradural and subcutaneus metastases were detected. These metastasis sites were first described for UESL.
ISSN:1930-0433
1930-0433
DOI:10.1016/j.radcr.2021.10.017