Atriofascicular Mahaim with Ebstein anomaly: A case report

We report a case of a 7‐year‐old girl with atriofascicular Mahaim (AFM) pathway concomitant with Ebstein's anomaly. The QRS wave showed left bundle branch block pattern on electrocardiogram. Holter electrocardiogram showed prolongation of the PR interval and QRS morphological change during sinu...

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Bibliographic Details
Published in:Journal of arrhythmia 2017-10, Vol.33 (5), p.508-510
Main Authors: Ueshima, Kazushi, Nakamura, Yoshihide, Takeno, Satoru, Miyake, Toshiharu, Takemura, Tsukasa
Format: Article
Language:English
Subjects:
Ablation
Atriofascicular Mahaim
Cardiac arrhythmia
Case Report
Case reports
Catheters
Conflicts of interest
Diagnosis
Ebstein anomaly
Electrocardiogram
Electrocardiography
Electrophysiology study
Heart failure
Patients
Radiofrequency catheter ablation
Sinuses
Tachycardia
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Summary:We report a case of a 7‐year‐old girl with atriofascicular Mahaim (AFM) pathway concomitant with Ebstein's anomaly. The QRS wave showed left bundle branch block pattern on electrocardiogram. Holter electrocardiogram showed prolongation of the PR interval and QRS morphological change during sinus tachycardia. An electrophysiological study demonstrated that the distal His potential appeared earlier than the proximal His potential, which suggested retrograde His conduction toward the atrioventricular node. Conduction from the Mahaim fiber to the His bundle was faster than that from the atrioventricular node towards the His bundle. The findings of this important case allowed a differential diagnosis between AFM and Wolff‐Parkinson‐White (WPW) syndrome.
ISSN:1880-4276
1883-2148
DOI:10.1016/j.joa.2017.06.007