Extra-Abdominal Desmoid Tumours : A Review of the Literature

Extra-abdominal desmoid lesions, otherwise known as aggressive fibromatosis, are slow-growing benign lesions which may be encountered in clinical practice. Recent controversies exist regarding their optimal treatment. Given their benign nature, is major debulking surgery justified, or is it worth ad...

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Bibliographic Details
Published in:Sarcoma 2012, Vol.2012 (2012), p.1-9
Main Authors: Molloy, A. P., Hutchinson, B., O'Toole, G. C.
Format: Article
Language:English
Online Access:Get full text
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Summary:Extra-abdominal desmoid lesions, otherwise known as aggressive fibromatosis, are slow-growing benign lesions which may be encountered in clinical practice. Recent controversies exist regarding their optimal treatment. Given their benign nature, is major debulking surgery justified, or is it worth administering chemotherapy for a disease process which unusually defies common teaching and responds to such medications? We present a literature review of this particular pathology discussing the aetiology, clinical presentation, and various current controversies in the treatment options.
ISSN:1357-714X
1369-1643