Pineoblastoma presenting in familial adenomatous polyposis (FAP): random association, FAP variant or Turcot syndrome?

Brain tumours which arise in combination with adenomatous polyposis are usually astrocytic tumours or medulloblastomas. An adult women with a pineoblastoma associated with familial adenomatous polyposis is presented. In regard to the neuro-epithelial origin of this tumour we propose that it should b...

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Bibliographic Details
Published in:British journal of neurosurgery 1998-12, Vol.12 (6), p.576-578
Main Authors: IKEDA, J., SAWAMURA, Y., VAN MEIR, E. G.
Format: Article
Language:English
Subjects:
Adenomatous Polyposis Coli - complications
Adenomatous Polyposis Coli - genetics
Adult
Biological and medical sciences
Brain
Brain Neoplasms - complications
Brain Neoplasms - genetics
Brain Tumour Familial Adenomatous Polyposis Pineal Neuroblastoma Turcot Syndrome
Female
Humans
Medical sciences
Neurology
Pedigree
Pineal Gland
Pinealoma - complications
Pinealoma - genetics
Syndrome
Tumors
Tumors of the nervous system. Phacomatoses
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Summary:Brain tumours which arise in combination with adenomatous polyposis are usually astrocytic tumours or medulloblastomas. An adult women with a pineoblastoma associated with familial adenomatous polyposis is presented. In regard to the neuro-epithelial origin of this tumour we propose that it should be included in the second category of brain tumour polyposis syndrome.
ISSN:0268-8697
1360-046X
DOI:10.1080/02688699844475