Mesenchymal Chondrosarcoma of the Orbit: A Report of Two Cases and Review of the Literature

Mesenchymal chondrosarcoma, an uncommon lesion in bone and extraskeletal tissue, is extremely rare in the orbit. Two cases of orbital mesenchymal chondrosarcoma in young adults presenting with proptosis and diminution of vision are reported. The diagnosis was established by histopathological examina...

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Bibliographic Details
Published in:Orbit (Amsterdam) 2008, Vol.27 (1), p.63-67
Main Authors: Kaur, Apjit, Kishore, Poonam, Agrawal, Ajai, Gupta, Aparna
Format: Article
Language:English
Subjects:
Adult
Antineoplastic Combined Chemotherapy Protocols - administration & dosage
Chondrosarcoma, Mesenchymal - pathology
Chondrosarcoma, Mesenchymal - therapy
Cyclophosphamide - administration & dosage
Dactinomycin - administration & dosage
exenteration
Extraskeletal mesenchymal chondrosarcoma
Female
Humans
Male
Neoplasm Recurrence, Local - therapy
Orbit Evisceration
Orbital Neoplasms - pathology
Orbital Neoplasms - therapy
orbital tumor
proptosis
Radiotherapy, Adjuvant
Reoperation
Vincristine - administration & dosage
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Summary:Mesenchymal chondrosarcoma, an uncommon lesion in bone and extraskeletal tissue, is extremely rare in the orbit. Two cases of orbital mesenchymal chondrosarcoma in young adults presenting with proptosis and diminution of vision are reported. The diagnosis was established by histopathological examination in both cases, which showed undifferentiated mesenchymal cells with islands of cartilage. Both patients underwent exenteration followed by chemotherapy and radiation therapy and are alive with healthy orbits after two years of follow-up.
ISSN:0167-6830
1744-5108
DOI:10.1080/01676830601169007