Aneurysms of the sinuses of Valsalva in Noonan's syndrome

A case of Noonan 's syndrome with aneurysmal dilatation of the sinuses of Valsalva is described. Enlargement of the left heart border on the postero-anterior chest radiograph was initially interpreted as dilatation of main pulmonary artery but aortography confirmed the presence of large aneurys...

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Bibliographic Details
Published in:European Heart Journal 1989, Vol.10 (2), p.190-193
Main Authors: MORGAN, J. M., COUPE, M. O., HONEY, M., MILLER, G. A. H.
Format: Report
Language:English
Subjects:
aneurysmal dilatation
connective tissue abnormality
Noonan's syndrome
sinuses of Valsalva
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Summary:A case of Noonan 's syndrome with aneurysmal dilatation of the sinuses of Valsalva is described. Enlargement of the left heart border on the postero-anterior chest radiograph was initially interpreted as dilatation of main pulmonary artery but aortography confirmed the presence of large aneurysms of two of the sinuses of Valsalva. Connective tissue abnormalities, known to occur in Noonan's syndrome, could be responsible for aortic abnormalities in this syndrome.
ISSN:0195-668X
1522-9645
DOI:10.1093/oxfordjournals.eurheartj.a059462