Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension

Superficial siderosis (SS) of the nervous system is a rare acquired condition related to hemosiderin deposits in subpial layers of the brain, brainstem, cerebellum, cranial nerves, and spinal cord, leading to brain iron-mediated neurodegeneration. The cardinal neurological features are slowly progre...

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Bibliographic Details
Published in:Case reports in neurology 2021-01, Vol.13 (1), p.9-16
Main Authors: Guimarães Rocha, Maria Sheila, Grangeiro Mirô, Hugo Salomão, Manfroi, Gregori, de Medeiros Dias, Arthur, Cardoso, Raphaella, Dozzi Brucki, Sonia Maria
Format: Article
Language:English
Subjects:
Ataxia
Case reports
ferritin
Headaches
Hemorrhage
Hypertension
intracranial hypertension
Magnetic resonance imaging
Medical imaging
Nervous system
neurodegeneration
neurosensorial deafness
Single Case – General Neurology
Single Case − General Neurology
Spinal cord
superficial siderosis
Trauma
Traumatic brain injury
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Summary:Superficial siderosis (SS) of the nervous system is a rare acquired condition related to hemosiderin deposits in subpial layers of the brain, brainstem, cerebellum, cranial nerves, and spinal cord, leading to brain iron-mediated neurodegeneration. The cardinal neurological features are slowly progressive hearing loss, ataxia, and pyramidal signs. Here we describe an atypical case of infratentorial SS evolving with acute intracranial hypertension in the absence of typical chronic signs.
ISSN:1662-680X
1662-680X
DOI:10.1159/000510847