Pulmonary Leukocytoclastic Vasculitis as an Initial Presentation of Myelodysplastic Syndrome

Systemic vasculitis involving the lung is a rare manifestation of myelodysplastic syndrome (MDS), and secondary vasculitis is considered to have poor prognosis. A 44-year-old man presented with fever and dyspnea of 1 month duration. A chest radiograph revealed bilateral multiple wedge shaped consoli...

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Published in:Tuberculosis and respiratory diseases 2016, 79(4), 367, pp.302-306
Main Authors: Lee, Seung Hyun, Kim, Jae Hyung, Park, Sejin, Won, Chang Youn, Lee, Joo-Hyun, Yi, Seong Yoon, Park, Hye Kyeong, Chang, Sun Hee, Jung, Hoon, Lee, Sung-Soon, Koo, Hyeon-Kyoung
Format: Article
Language:English
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Case Report
내과학
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Summary:Systemic vasculitis involving the lung is a rare manifestation of myelodysplastic syndrome (MDS), and secondary vasculitis is considered to have poor prognosis. A 44-year-old man presented with fever and dyspnea of 1 month duration. A chest radiograph revealed bilateral multiple wedge shaped consolidations. In addition, the results of a percutaneous needle biopsy for non-resolving pneumonia were compatible with pulmonary vasculitis. Bone marrow biopsy was performed due to the persistence of unexplained anemia and the patient was diagnosed with MDS. We reported a case of secondary vasculitis presenting as non-resolving pneumonia, later diagnosed as paraneoplastic syndrome of undiagnosed MDS. The cytopenia and vasculitis improved after a short course of glucocorticoid treatment, and there was no recurrence despite the progression of underlying MDS.
ISSN:1738-3536
2005-6184
DOI:10.4046/trd.2016.79.4.302