A Case of IgG4-Related Disease Presenting as Massive Pleural Effusion and Thrombophlebitis

Immunoglobulin (Ig) G4-related disease is a recently recognized systemic fibroinflammatory condition characterized by a lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells with elevated circulating levels of IgG4. The disease can either be localized to one or two organs, or present as di...

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Published in:Tuberculosis and respiratory diseases 2014, 76(4), 351, pp.179-183
Main Authors: Choi, Jong Hyun, Sim, Jae Kyeom, Oh, Jee Youn, Lee, Eun Joo, Hur, Gyu Young, Lee, Seung Heon, Lee, Sung Yong, Kim, Je Hyeong, Lee, Sang Yeub, Shin, Chol, Shim, Jae Jeong, In, Kwang Ho, Kang, Kyung Ho, Min, Kyung Hoon
Format: Article
Language:English
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Case Report
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Summary:Immunoglobulin (Ig) G4-related disease is a recently recognized systemic fibroinflammatory condition characterized by a lymphoplasmacytic infiltrate rich in IgG4-positive plasma cells with elevated circulating levels of IgG4. The disease can either be localized to one or two organs, or present as diffuse multi-organ disease. Furthermore, lesions in different organs can present simultaneously or metachronously. In the pulmonary manefestations, lesions associated with IgG4-related disease have been described in the lung parenchyma, airways and pleura, as well as the mediastinum. We report a case of IgG4-related disease presenting as massive pleural effusion and thrombophlebitis.
ISSN:1738-3536
2005-6184
DOI:10.4046/trd.2014.76.4.179