Loeys-Dietz Syndrome 환아에서 대동맥판막 역류증 수술의 마취 관리

Loeys-Dietz Syndrome (LDS) is a recently described autosomal dominant aortic aneurysm syndrome with widespread systemic involvement. It is characterized by the triad of 1) arterial tortuosity and aneurysms, 2) hypertelorism, and 3) bifid uvula or cleft palate. A 12-year-old boy with LDS was schedule...

Full description

Saved in:
Bibliographic Details
Published in:Korean journal of anesthesiology 2009, 57(3), , pp.371-375
Main Authors: 김성협, Seong Hyop Kim, 백승우, Seung Woo Baek, 권원경, Won Kyoung Kwon, 김덕경, Duk Kyung Kim, 윤태균, Tae Gyoon Yoon, 임정애, Jeong Ae Lim, 우남식, Nam Sik Woo, 김태엽, Tae Yop Kim
Format: Article
Language:Korean
Subjects:
Anesthetic managements
Aortic valve regurgitation
Loeys-Dietz Syndrome
마취과학
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Loeys-Dietz Syndrome (LDS) is a recently described autosomal dominant aortic aneurysm syndrome with widespread systemic involvement. It is characterized by the triad of 1) arterial tortuosity and aneurysms, 2) hypertelorism, and 3) bifid uvula or cleft palate. A 12-year-old boy with LDS was scheduled to undergo correction of aortic valve regurgitation due to aortic annuloectasia. We report our clinical experiences of a case of LDS patient with brief review of related literatures and relevant anesthetic problems. (Korean J Anesthesiol 2009;57:371∼5)
ISSN:2005-6419
2005-7563