C64 PEDIATRIC CASE REPORTS: BPD AND CONGENITAL LUNG DISEASES: Congenital Pulmonary Lymphangiectasia With Cd4 Lymphopenia Presenting In Adulthood

Congenital pulmonary lymphangiectasia (CPL) is a rare disorder with a high mortality rate that usually presents with severe respiratory distress at birth often requiring mechanical ventilation. Treatment included pneumocystis prophylaxis, bronchial hygiene with an oscillatory positive pressure flutt...

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Bibliographic Details
Published in:American journal of respiratory and critical care medicine 2017-01, Vol.195
Main Authors: Stroh, G, Dulohery, M
Format: Article
Language:English
Subjects:
Pediatrics
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Summary:Congenital pulmonary lymphangiectasia (CPL) is a rare disorder with a high mortality rate that usually presents with severe respiratory distress at birth often requiring mechanical ventilation. Treatment included pneumocystis prophylaxis, bronchial hygiene with an oscillatory positive pressure flutter valve, medium-chain triglyceride diet, and continuation of formoterol/mometasone with the addition of albuterol.
ISSN:1073-449X
1535-4970