Angioma of the face: about two cases including one revealing Sturge Weber and Krabbe syndrome

Sturge Weber and Krabbe syndrome or Sturge weber Syndrome (SWS) is a rare and sporadic disease. It associates with a variety of degrees a flat facial skin angioma in the V1 territory of the trigeminal, a pial angioma and a choroidal angioma all in the one side. The neurological involvement of epilep...

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Bibliographic Details
Published in:Nasza dermatologia online 2017-01, Vol.8 (1), p.70-74
Main Authors: Tiemtoré-Kambou, Bénilde Marie Ange, Ouédraogo, Nomtondo Amina, Ndé-Ouédraogo, Nina-Astrid, Traoré, Fagnima, Ouédraogo, Pakisba Ali, Dao, Ben Aziz, Ouattara, Boubacar, Zanga, Moussa, Diallo, Ousséini, Cissé, Rabiou
Format: Article
Language:English
Subjects:
Case reports
Health surveillance
Localization
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Summary:Sturge Weber and Krabbe syndrome or Sturge weber Syndrome (SWS) is a rare and sporadic disease. It associates with a variety of degrees a flat facial skin angioma in the V1 territory of the trigeminal, a pial angioma and a choroidal angioma all in the one side. The neurological involvement of epileptic seizures in fact all the gravity. The authors report two cases of angiomas plane of the face. The first case presents a complete association of the 3 signs in a 5 year old child. The second case presents an association of angioma and choroidal involvement without cerebral damage to imaging in a 25-year-old adult. They thus highlight the interest of imaging examinations in particular MRI in the diagnosis through the classification and follow-up of this pathology.
ISSN:2081-9390
2081-9390
DOI:10.7241/ourd.20171.19