Hypoplastic left heart syndrome with parchment left ventricle: A rare perinatal autopsy case report

Hypoplastic left heart syndrome (HLHS) refers to the abnormal development of the left-sided cardiac structures, resulting in obstruction to blood flow from the left ventricular outflow tract. In addition, the syndrome includes underdevelopment of the left ventricle, aorta, and aortic arch, as well a...

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Bibliographic Details
Published in:Journal of medicine, radiology, pathology and surgery radiology, pathology and surgery, 2015-03, Vol.1 (2), p.26-28
Main Authors: Chatura, K. R., Neethu, G. V., Mavintop, K. S.
Format: Article
Language:English
Subjects:
Births
Case reports
Congenital diseases
Electrocardiography
Prenatal development
Online Access:Get full text
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Summary:Hypoplastic left heart syndrome (HLHS) refers to the abnormal development of the left-sided cardiac structures, resulting in obstruction to blood flow from the left ventricular outflow tract. In addition, the syndrome includes underdevelopment of the left ventricle, aorta, and aortic arch, as well as mitral atresia or stenosis. The syndrome can be diagnosed by fetal echocardiography between 18 and 22 weeks of gestation. This is a fetal autopsy case report of HLHS, which was diagnosed on ultrasonography and medically terminated at 20 weeks of gestation. The autopsy and histopathological findings are discussed in detail. Some important aspects of epidemiology, prenatal diagnosis, and current literature on HLHS are highlighted.
ISSN:2395-2075
2395-2075
DOI:10.15713/ins.jmrps.12