First presentation of Sneddon-Wilkinson disease with unexpectedimmunoglobulin A gammopathy: A case report and review of theliterature

We present a case of Sneddon-Wilkinson disease in a 52-year-old female at herfirst presentation to dermatology. Outlined in the case are variousinvestigations undertaken at this initial presentation, including rheumatologicand hematologic malignancy markers, which identified immunoglobulin Agammopat...

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Published in:SAGE open medical case reports 2019-01, Vol.7
Main Authors: Mayba, Julia N, Nicole, Hawkins C
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description We present a case of Sneddon-Wilkinson disease in a 52-year-old female at herfirst presentation to dermatology. Outlined in the case are variousinvestigations undertaken at this initial presentation, including rheumatologicand hematologic malignancy markers, which identified immunoglobulin Agammopathy. The systemic and topical therapies used to treat thepatient’s condition are described, as well as her response to thesetreatments. In this discussion, we explain the epidemiology, pathophysiology,and clinical presentation of Sneddon-Wilkinson disease. Various medicalconditions having known association with Sneddon-Wilkinson disease arediscussed, including immunoglobulin A or immunoglobulin G monoclonalgammopathies and lymphoproliferative disorders. A comprehensive differentialdiagnosis for Sneddon-Wilkinson disease is provided, including immunoglobulin Apemphigus, acute generalized exanthematous pustulosis and pustular psoriasis,among others. We describe the systemic and topical therapy options for thetreatment of Sneddon-Wilkinson disease, of which first line treatment issystemic dapsone. This patient serves as an excellent case of Sneddon-Wilkinsondisease with unexpected immunoglobulin A gammopathy.
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Immunoglobulins
title First presentation of Sneddon-Wilkinson disease with unexpectedimmunoglobulin A gammopathy: A case report and review of theliterature
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