AUTOSOMAL DOMINANT HYPER IGESYNDROME : A CASE REPORT OF TWO PATIENTS

ABSTRACT Recently we came across two male patients with Hyper IgE type immune deficiency (HIES/Job's syndrome), a primary immune deficiency disorder characterized by abnormally raised serum levels of IgE and repeated childhood infections. In our hospital in pediatrics and nursery, acquired immu...

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Published in:Pakistan Armed Forces medical journal 2020-02 (1), p.S188
Main Authors: Gillani, Saima, Aziz, Farida, Burhan Ali Danish, Attia Iqbal, Muhammad Junaid Khan
Format: Article
Language:English
Subjects:
Advertising executives
Age
Antibiotics
Antibodies
Case reports
Children & youth
Dermatitis
Disease prevention
Ear diseases
Health aspects
Immunodeficiency
Immunoglobulin E
Immunoglobulins
Infection
Infections
Lung diseases
Lymphatic system
Methicillin
Mutation
Neutrophils
Pneumonia
Rash
Recurrence (Disease)
Respiratory tract diseases
Resveratrol
Scoliosis
Staphylococcal infections
Teeth
Viral infections
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creator Gillani, Saima
Aziz, Farida
Burhan Ali Danish
Attia Iqbal
Muhammad Junaid Khan
description ABSTRACT Recently we came across two male patients with Hyper IgE type immune deficiency (HIES/Job's syndrome), a primary immune deficiency disorder characterized by abnormally raised serum levels of IgE and repeated childhood infections. In our hospital in pediatrics and nursery, acquired immunodeficiency secondary to severe malnutrition, prolonged steroid therapy, nephrotic syndrome, aplastic anemia, leishmaniasis, leukemias and other malignancies is more common as compared to inherited causes.
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source Nexis UK; Publicly Available Content (ProQuest)
subjects Advertising executives
Age
Antibiotics
Antibodies
Case reports
Children & youth
Dermatitis
Disease prevention
Ear diseases
Health aspects
Immunodeficiency
Immunoglobulin E
Immunoglobulins
Infection
Infections
Lung diseases
Lymphatic system
Methicillin
Mutation
Neutrophils
Pneumonia
Rash
Recurrence (Disease)
Respiratory tract diseases
Resveratrol
Scoliosis
Staphylococcal infections
Teeth
Viral infections
title AUTOSOMAL DOMINANT HYPER IGESYNDROME : A CASE REPORT OF TWO PATIENTS
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