G21(P) Ebstein’s anomaly in the neonatal period is associated with very poor prognosis – a 10 year experience

IntroductionEbstein’s anomaly is a rare form of congenital heart disease (CHD), occurring in less than 1% of patients with CHD. With advances in Fetal Medicine and Cardiology, Ebstein’s anomaly is being diagnosed antenatally. The literature highlights that it can be difficult to predict the prognosi...

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Bibliographic Details
Published in:Archives of disease in childhood 2020-10, Vol.105 (Suppl 1), p.A4-A5
Main Authors: Jagga, M, Nijjar, I, Desai, T, Rasiah, SV
Format: Article
Language:English
Subjects:
Cardiology
Cardiovascular disease
Cardiovascular diseases
Congenital diseases
Congenital Impairments
Coronary artery disease
Diagnosis
Down Syndrome
Edema
Fetuses
Heart diseases
Hydrops fetalis
Hypertension
Hypothermia
Infants
Intensive care
Intubation
Medical prognosis
Neonatal care
Neonates
Newborn babies
Pediatrics
Premature birth
Prognosis
Survival
Trisomy
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Summary:IntroductionEbstein’s anomaly is a rare form of congenital heart disease (CHD), occurring in less than 1% of patients with CHD. With advances in Fetal Medicine and Cardiology, Ebstein’s anomaly is being diagnosed antenatally. The literature highlights that it can be difficult to predict the prognosis particularly during the neonatal period.AimsOur aim was to review the neonatal outcomes of babies with Ebstein’s anomaly admitted to our tertiary neonatal intensive care unit (NICU).MethodWe retrospectively identified all babies admitted to the NICU with a documented diagnosis of Ebstein’s anomaly between 01/04/2009 and 31/04/2019. Their outcome data was collected using electronic patient records (BadgerNet).ResultsIn the last 10 years, 11 babies had a documented diagnosis of Ebstein’s anomaly. Ten of these were antenatally diagnosed. Four were born prematurely (
ISSN:0003-9888
1468-2044
DOI:10.1136/archdischild-2020-rcpch.10