Imaging of Pediatric Desmoplastic Small–Round-Cell Tumor with Pathologic Correlation

Desmoplastic small–round-cell tumors are rare aggressive malignancies that belong to the “small round blue cell” tumor family. They predominantly affect the abdomen in adolescent and young adult males. Computed tomography is currently the modality of choice both for diagnosis and follow-up assessmen...

Full description

Saved in:
Bibliographic Details
Published in:Current problems in diagnostic radiology 2013, Vol.42 (1), p.26-32
Main Authors: Iyer, Ramesh S., MD, Schaunaman, Gwen, MD, Pruthi, Sumit, MD, Finn, Laura S., MD
Format: Article
Language:English
Subjects:
Abdominal Neoplasms - diagnosis
Adolescent
Antineoplastic Combined Chemotherapy Protocols - therapeutic use
Chemotherapy, Adjuvant
Child
Child, Preschool
Desmoplastic Small Round Cell Tumor - diagnosis
Desmoplastic Small Round Cell Tumor - diagnostic imaging
Desmoplastic Small Round Cell Tumor - mortality
Desmoplastic Small Round Cell Tumor - pathology
Diagnosis, Differential
Female
Humans
Internal Medicine
Male
Peritoneal Neoplasms - diagnosis
Peritoneal Neoplasms - diagnostic imaging
Peritoneal Neoplasms - mortality
Peritoneal Neoplasms - pathology
Prognosis
Radiology
Tomography, X-Ray Computed
Young Adult
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Desmoplastic small–round-cell tumors are rare aggressive malignancies that belong to the “small round blue cell” tumor family. They predominantly affect the abdomen in adolescent and young adult males. Computed tomography is currently the modality of choice both for diagnosis and follow-up assessment. In this review, the authors provide a concise yet comprehensive discussion of this condition with emphasis on the imaging findings. Pathologic correlation, differential diagnostic considerations, and treatment will also be presented.
ISSN:0363-0188
1535-6302
DOI:10.1067/j.cpradiol.2012.05.004