Hepatic mesenchymal hamartoma in a neonate with a Bochdalek diaphragmatic hernia: A case report

Abstract The Bochdalek diaphragmatic hernia (BDH) is a common birth defect that is associated with other congenital malformations. Hepatic mesenchymal hamartoma (HMH) is the second most common benign hepatic tumor in children. The association between BDH and HMH or ectopic hepatic tissue is uncommon...

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Bibliographic Details
Published in:Journal of pediatric surgery 2012-11, Vol.47 (11), p.e45-e48
Main Authors: Ortiz Otero, Angela, de Prada Vicente, Inmaculada, Gutierrez Herrera, Jair, Azorín Cuadrilleros, Daniel
Format: Article
Language:English
Subjects:
Choristoma - complications
Choristoma - congenital
Choristoma - diagnosis
Congenital diaphragmatic hernia
Diaphragm - pathology
Female
Hamartoma - complications
Hamartoma - congenital
Hamartoma - diagnosis
Hepatic mesenchymal hamartoma
Hernia, Diaphragmatic - complications
Hernia, Diaphragmatic - diagnosis
Hernias, Diaphragmatic, Congenital
Humans
Infant, Newborn
Liver
Liver Diseases - complications
Liver Diseases - congenital
Liver Diseases - diagnosis
Liver tumor
Pediatrics
Surgery
Undifferentiated embryonal sarcoma
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Summary:Abstract The Bochdalek diaphragmatic hernia (BDH) is a common birth defect that is associated with other congenital malformations. Hepatic mesenchymal hamartoma (HMH) is the second most common benign hepatic tumor in children. The association between BDH and HMH or ectopic hepatic tissue is uncommon. We report a case of a female newborn with a left BDH that at surgery was incidentally found to have a tumor of 3.5 cm in maximum dimension with a serous muscular membrane. The histopathological study revealed vascular–mesenchymal stroma with bile ducts entrapped and peripheral normal hepatic tissue. These findings correlate with the diagnosis of hepatic mesenchymal hamartoma (HMH) in ectopic hepatic tissue. Our objective is to report a case of a rare association between HMH and BDH as well as discuss its differential diagnosis.
ISSN:0022-3468
1531-5037
DOI:10.1016/j.jpedsurg.2012.07.053