Repair of a Complex Thoracic Aneurysm From Relapsing Polychondritis

A 29-year-old female with a history of relapsing polychondritis (RP) and open repair of a proximal descending thoracic aneurysm presented with 2 areas of asymptomatic thoracic aortic aneurysmal dilatation. The patient returned 3 months later with symptomatic aneurysm expansion, and she underwent asc...

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Bibliographic Details
Published in:Vascular and endovascular surgery 2013-07, Vol.47 (5), p.387-389
Main Authors: Jacobs, Chad E, March, Robert J., Hunt, Peter J., Rivera, Aksim G., Cavanagh, Sherry, McCarthy, Walter J
Format: Article
Language:English
Subjects:
Adult
Aortic Aneurysm, Thoracic - diagnosis
Aortic Aneurysm, Thoracic - etiology
Aortic Aneurysm, Thoracic - surgery
Aortography - methods
Blood Vessel Prosthesis Implantation
Endovascular Procedures
Female
Humans
Polychondritis, Relapsing - complications
Tomography, X-Ray Computed
Treatment Outcome
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Summary:A 29-year-old female with a history of relapsing polychondritis (RP) and open repair of a proximal descending thoracic aneurysm presented with 2 areas of asymptomatic thoracic aortic aneurysmal dilatation. The patient returned 3 months later with symptomatic aneurysm expansion, and she underwent ascending aortic arch replacement. She subsequently underwent staged endovascular repair of the distal descending thoracic aorta. RP is a rare disorder with an incidence of 3.5 per million persons annually, 4% to 7% of whom develop aneurysmal disease. Because of the aneurysmal potential of this disease, it is important for vascular surgeons to be aware of its presentation and treatment. To our knowledge, this is the first reported case describing endovascular technique to treat such a patient.
ISSN:1538-5744
1938-9116
DOI:10.1177/1538574413488459