A Rare Association of Pulmonary Hypertension and Dextrocardia with Poland Syndrome

Poland syndrome is a rare congenital abnormality with an estimated incidence of 1 in 20,000 to 1 in 30,000 live births. We report and discuss this rare combination of pulmonary hypertension and dextrocardia with Poland syndrome. This case report also highlights the underlying pathogenetic mechanisms...

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Bibliographic Details
Published in:Heart, lung & circulation lung & circulation, 2013-09, Vol.22 (9), p.778-780
Main Authors: Raval, Jwalant, MBBS, Nagaraja, Vinayak, MBBS, Burgess, David, PhD, FRACP, Eshoo, Suzanne, PhD, FRACP, Sadick, Norman, PhD, FRACP, Denniss, A. Robert, MD, MSc, FRACP
Format: Article
Language:English
Subjects:
Cardiovascular
Dextrocardia
Dextrocardia - complications
Dextrocardia - diagnosis
Diagnostic Errors
Humans
Hypertension, Pulmonary - complications
Hypertension, Pulmonary - diagnosis
Male
Middle Aged
Myocardial Ischemia - complications
Myocardial Ischemia - diagnosis
Poland syndrome
Poland Syndrome - complications
Poland Syndrome - diagnosis
Pulmonary hypertension
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Summary:Poland syndrome is a rare congenital abnormality with an estimated incidence of 1 in 20,000 to 1 in 30,000 live births. We report and discuss this rare combination of pulmonary hypertension and dextrocardia with Poland syndrome. This case report also highlights the underlying pathogenetic mechanisms during foetal development and the potential to misdiagnose cardiac ischaemia in a patient with an anatomic anomaly.
ISSN:1443-9506
1444-2892
DOI:10.1016/j.hlc.2013.03.076