Esthesioneuroblastoma as an Unusual Cause for Dystopia

Abstract Esthesioneuroblastoma, also known as olfactory neuroblastoma, is an uncommon malignant neoplasm arising from the olfactory epithelium in the roof of the nasal cavity. There are very few case reports published worldwide. The common presenting symptoms of Esthesioneuroblastoma are unilateral...

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Bibliographic Details
Published in:Orbit (Amsterdam) 2013-12, Vol.32 (6), p.392-394
Main Authors: Kamath, Vijna B., Sowmya, V., Ballal, Chandra Kumar, Mendonca, Norman
Format: Article
Language:English
Subjects:
Combined Modality Therapy
Craniotomy
Diagnosis, Differential
Esthesioneuroblastoma, Olfactory - diagnosis
Esthesioneuroblastoma, Olfactory - radiotherapy
Esthesioneuroblastoma, Olfactory - surgery
Exophthalmos
Eye Abnormalities - diagnosis
Humans
Magnetic Resonance Imaging
Male
Nasal Cavity - pathology
Nose Neoplasms - diagnosis
Nose Neoplasms - radiotherapy
Nose Neoplasms - surgery
Orbit - abnormalities
Tomography, X-Ray Computed
Young Adult
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Summary:Abstract Esthesioneuroblastoma, also known as olfactory neuroblastoma, is an uncommon malignant neoplasm arising from the olfactory epithelium in the roof of the nasal cavity. There are very few case reports published worldwide. The common presenting symptoms of Esthesioneuroblastoma are unilateral nasal obstruction (70%), epistaxis (50%), anosmia, rhinorrhoea, facial pain, headache, excessive lacrimation and rarely proptosis and visual disturbance. Apart from being locally aggressive, it metastasizes by haematogenous and lymphatic routes. We report an extremely rare case of esthesioneuroblastoma in a 20-year-old man with orbital involvement presenting as dystopia. This rare tumour should be considered in the differential diagnosis for young patients presenting to ophthalmic outpatient department with dystopia.
ISSN:0167-6830
1744-5108
DOI:10.3109/01676830.2013.833252