Heart Failure Due to “Disappearing” Aortic Valve in Hypoplastic Left Heart Syndrome

We present the unusual case of a “disappearing” aortic valve in an infant with hypoplastic left heart syndrome (mitral and aortic stenosis) that underwent Norwood palliation at birth and subsequently a Glenn operation. Angiographic images at the time of operation showed no apparent insufficiency of...

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Bibliographic Details
Published in:World journal for pediatric & congenital heart surgery 2014-04, Vol.5 (2), p.334-337
Main Authors: Loftus, Patrick D., Erickson, Lance K., Everitt, Melanie D., Kaza, Aditya K.
Format: Article
Language:English
Subjects:
Aortic Valve - diagnostic imaging
Aortic Valve - microbiology
Aortic Valve - pathology
Aortic Valve - physiopathology
Aortic Valve Insufficiency - complications
Aortic Valve Insufficiency - physiopathology
Coronary Angiography
Dilatation, Pathologic
Fibrosis
Heart Failure - etiology
Heart Failure - surgery
Heart Transplantation
Humans
Hypoplastic Left Heart Syndrome - complications
Hypoplastic Left Heart Syndrome - physiopathology
Infant, Newborn
Male
Myocardium - pathology
Ultrasonography
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Summary:We present the unusual case of a “disappearing” aortic valve in an infant with hypoplastic left heart syndrome (mitral and aortic stenosis) that underwent Norwood palliation at birth and subsequently a Glenn operation. Angiographic images at the time of operation showed no apparent insufficiency of the native aortic valve. Over the course of 14 months following operation, the patient developed significant cardiomegaly with a workup revealing severe native aortic valve insufficiency. Following orthotopic heart transplantation, examination of the explanted heart revealed a complete absence of native aortic valve leaflets.
ISSN:2150-1351
2150-136X
DOI:10.1177/2150135113512137