Congenital subclavian steal syndrome with multiple cerebellar infarctions caused by an atypical circumflex retroesophageal right aortic arch with atretic aberrant left subclavian artery

A right-sided aortic arch is a rare anomaly with an incidence of 0.1% worldwide and is usually associated with a mirror image of all supra-aortic branches or an aberrant left subclavian artery. The latter is often associated with a Kommerell diverticulum, although it can rarely be hypoplastic or atr...

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Bibliographic Details
Published in:Journal of vascular surgery 2014-09, Vol.60 (3), p.776-779
Main Authors: Mamopoulos, Apostolos T., MD, Luther, Bernd, PhD
Format: Article
Language:English
Subjects:
Aneurysm - complications
Aneurysm - diagnosis
Aneurysm - surgery
Aorta, Thoracic - abnormalities
Aortography - methods
Cardiovascular Abnormalities - complications
Cardiovascular Abnormalities - diagnosis
Cardiovascular Abnormalities - surgery
Cerebral Angiography - methods
Cerebral Infarction - diagnosis
Cerebral Infarction - etiology
Deglutition Disorders - complications
Deglutition Disorders - diagnosis
Deglutition Disorders - surgery
Humans
Magnetic Resonance Angiography
Male
Middle Aged
Subclavian Artery - abnormalities
Subclavian Artery - surgery
Subclavian Steal Syndrome - diagnosis
Subclavian Steal Syndrome - etiology
Subclavian Steal Syndrome - surgery
Surgery
Tomography, X-Ray Computed
Treatment Outcome
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Description
Summary:A right-sided aortic arch is a rare anomaly with an incidence of 0.1% worldwide and is usually associated with a mirror image of all supra-aortic branches or an aberrant left subclavian artery. The latter is often associated with a Kommerell diverticulum, although it can rarely be hypoplastic or atretic and lead to congenital subclavian steal. In most patients, the situation is well-tolerated. In this report, we present a case of subclavian steal syndrome with multiple cerebellar infarcts in a patient with an atypical right-sided aortic arch and an atretic aberrant left subclavian artery arising from a left-sided descending thoracic aorta.
ISSN:0741-5214
1097-6809
DOI:10.1016/j.jvs.2013.06.086