Nodular Cystic Fat Necrosis with Calcification in a Patient with Juvenile Dermatomyositis

Nodular cystic fat necrosis is a rare, benign form of encapsulated fat necrosis with distinct histology, characterized by cystic fat necrosis with lipomembranous changes and, in later stages, calcification. We report the case of a 7‐year‐old child with juvenile dermatomyositis who presented with thr...

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Bibliographic Details
Published in:Pediatric dermatology 2014-09, Vol.31 (5), p.588-590
Main Authors: Ferenczi, Katalin, Berke, Adrienne, Makkar, Hanspaul S.
Format: Article
Language:English
Subjects:
Biopsy
Calcinosis - etiology
Calcinosis - pathology
Calcinosis - therapy
Child
Dermatologic Agents - therapeutic use
Dermatomyositis - complications
Dermatomyositis - pathology
Dermatomyositis - therapy
Drug Therapy, Combination
Enzyme Inhibitors - therapeutic use
Fat Necrosis - etiology
Fat Necrosis - pathology
Fat Necrosis - therapy
Female
Glucocorticoids - therapeutic use
Humans
Hydroxychloroquine - therapeutic use
Magnetic Resonance Imaging
Methotrexate - therapeutic use
Prednisone - therapeutic use
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Summary:Nodular cystic fat necrosis is a rare, benign form of encapsulated fat necrosis with distinct histology, characterized by cystic fat necrosis with lipomembranous changes and, in later stages, calcification. We report the case of a 7‐year‐old child with juvenile dermatomyositis who presented with three asymptomatic, firm, mobile nodules on the arms and neck. Histology was consistent with nodular cystic fat necrosis with prominent calcification. This is an unusual presentation of this entity because it has never been previously reported in association with juvenile dermatomyositis.
ISSN:0736-8046
1525-1470
DOI:10.1111/pde.12363