Liver Transplantation in a Patient With Clinical Manifestations of Cryptogenic Cirrhosis: A Case Report of Hepar Lobatum as a Primary Liver Condition

Abstract Background This article reports a case of hepar lobatum, a peculiar and rare type of liver deformity, originally described in association with infectious or parasitic diseases and with malignancies. Case Report We have described a 42-year-old woman with this disorder, which was unrelated to...

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Bibliographic Details
Published in:Transplantation proceedings 2014-09, Vol.46 (7), p.2433-2436
Main Authors: Bonfitto, J.F.L, Mattosinho, T.J.A.P, Neves, I, Ataide, E.C, Boin, I.F.S.F, Stucchi, R.S.B, Martins, D.L, Escanhoela, C.A.F
Format: Article
Language:English
Subjects:
Adult
Diagnosis, Differential
Female
Humans
Hypertension, Portal - etiology
Hypertension, Portal - surgery
Liver - pathology
Liver Cirrhosis - congenital
Liver Cirrhosis - diagnosis
Liver Transplantation
Surgery
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Summary:Abstract Background This article reports a case of hepar lobatum, a peculiar and rare type of liver deformity, originally described in association with infectious or parasitic diseases and with malignancies. Case Report We have described a 42-year-old woman with this disorder, which was unrelated to the known conditions and referred for liver transplantation for having clinical manifestations of cirrhosis, portal hypertension, and impaired hepatic function. Conclusions The observed histologic pattern suggests that hepar lobatum could be, in some patients, the effect of a primary process of hamartomatous origin involving the organ vascular supply.
ISSN:0041-1345
1873-2623
DOI:10.1016/j.transproceed.2013.09.057