Neuromuscular disease: respiratory clinical assessment and follow-up

Patients with neuromuscular disease are an important group at risk of frequently suffering acute or chronic respiratory failure, which is their main cause of death. They require follow-up by a pediatric respiratory medicine specialist from birth or diagnosis in order to confirm the diagnosis and tre...

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Published in:Anales de pediatría (Barcelona, Spain : 2003) Spain : 2003), 2014-10, Vol.81 (4), p.258.e1-258.e17
Main Authors: Martínez Carrasco, C, Villa Asensi, J R, Luna Paredes, M C, Osona Rodríguez de Torres, F B, Peña Zarza, J A, Larramona Carrera, H, Costa Colomer, J
Format: Article
Language:Spanish
Subjects:
Child
Deglutition Disorders - etiology
Follow-Up Studies
Humans
Neuromuscular Diseases - classification
Neuromuscular Diseases - complications
Respiration Disorders - diagnosis
Respiration Disorders - etiology
Spirometry
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Summary:Patients with neuromuscular disease are an important group at risk of frequently suffering acute or chronic respiratory failure, which is their main cause of death. They require follow-up by a pediatric respiratory medicine specialist from birth or diagnosis in order to confirm the diagnosis and treat any respiratory complications within a multidisciplinary context. The ventilatory support and the cough assistance have improved the quality of life and long-term survival for many of these patients. In this paper, the authors review the pathophysiology, respiratory function evaluation, sleep disorders, and the most frequent respiratory complications in neuromuscular diseases. The various treatments used, from a respiratory medicine point of view, will be analyzed in a next paper.
ISSN:1695-9531
DOI:10.1016/j.anpedi.2014.02.024