Ectopia cordis: A rare congenital anomaly

Ectopia cordis (EC) is a rare congenital anomaly associated with the heart positioned outside of the thoracic cavity either partially or completely. The ectopic heart can be found along a spectrum of anatomical locations, including the cervical, thoracic and abdominal regions and in most cases, it p...

Full description

Saved in:
Bibliographic Details
Published in:Clinical anatomy (New York, N.Y.) N.Y.), 2014-11, Vol.27 (8), p.1193-1199
Main Authors: Gabriel, Abigail, Donnelly, Joseph, Kuc, Alexander, Good, Daniel, Doros, Gabriela, Matusz, Petru, loukas, marios
Format: Article
Language:English
Subjects:
abdominal
cervical
congenital cardiac anomaly
ectopia cordis
Ectopia Cordis - embryology
Ectopia Cordis - history
Ectopia Cordis - surgery
History, 17th Century
History, 18th Century
History, 19th Century
History, 20th Century
History, 21st Century
Humans
Rare Diseases
thoracoabdominal
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Ectopia cordis (EC) is a rare congenital anomaly associated with the heart positioned outside of the thoracic cavity either partially or completely. The ectopic heart can be found along a spectrum of anatomical locations, including the cervical, thoracic and abdominal regions and in most cases, it protrudes outside the chest through a split sternum. Although the first case of EC was identified during the early 1600s only 91 cases have been reported since then in the literature. This review will discuss the history and prevalence of EC, its etiology, morphology, presentation and symptoms, complications, diagnosis, treatment and management and prognosis. Clin. Anat. 27:1193–1199, 2014. © 2014 Wiley Periodicals, Inc.
ISSN:0897-3806
1098-2353
DOI:10.1002/ca.22402