Management of congenital cartilaginous sleeve trachea in children

Abstract Aims Children with congenital tracheal cartilaginous sleeve may present to otolaryngology services with airway problems. We wish to describe our overall management in a series of four children with this very rare anomaly. Methods Retrospective case note review of children diagnosed with con...

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Bibliographic Details
Published in:International journal of pediatric otorhinolaryngology 2014-11, Vol.78 (11), p.2011-2014
Main Authors: Hamilton, Jane, Clement, W. Andrew, Kubba, Haytham
Format: Article
Language:English
Subjects:
Acrocephalosyndactylia - diagnosis
Cartilage - abnormalities
Cartilage - surgery
Cartilaginous
Child
Craniosynostosis
Esophagus - abnormalities
Female
Humans
Hypertelorism - diagnosis
Hypospadias - diagnosis
Infant
Laryngoplasty
Male
Opitz
Otolaryngology
Pediatrics
Pfeiffer's
Retrospective Studies
Sleeve
Trachea
Trachea - abnormalities
Trachea - surgery
Tracheostomy
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Summary:Abstract Aims Children with congenital tracheal cartilaginous sleeve may present to otolaryngology services with airway problems. We wish to describe our overall management in a series of four children with this very rare anomaly. Methods Retrospective case note review of children diagnosed with congenital tracheal cartilaginous sleeve presenting to our department between 2006 and 2014. Results Four patients were seen. One had Opitz G syndrome, two had Pfeiffers syndrome and one had no associated anomalies. Two children were successfully managed with laryngeal reconstruction using an anterior costal cartilage graft, while the third and fourth required a short period of tracheostomy only. All four are well and currently asymptomatic from an airway point of view. Conclusion Congenital tracheal cartilaginous sleeve is a very rare and potentially challenging problem. Otolaryngologists should be aware that it can occur in children with syndromes other than craniosynostosis (and indeed, those with no syndrome) and that it can be successfully treated using established airway management techniques. Ethical approval Registered with Clinical Governance Committee.
ISSN:0165-5876
1872-8464
DOI:10.1016/j.ijporl.2014.08.031