Osteomyelitis of the mandible and dysosteosclerosis

Dysosteosclerosis is a rare genetic disorder with a poor prognosis. It is an osteochondrodysplasia similar to osteopetrosis but it is typically characterized by platyspondyly and expanded metaphyses. It shows complications such as compression of cranial nerves, especially the optic nerve, hematologi...

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Bibliographic Details
Published in:Archives de pédiatrie : organe officiel de la Société française de pédiatrie 2015-11, Vol.22 (11), p.1154-1156
Main Authors: Kojmane, W, Chaouki, S, Abourazzak, S, Hida, M, Fikri, G, Boubou, M, Tizniti, S
Format: Article
Language:fre
Subjects:
Child, Preschool
Cutaneous Fistula - microbiology
Female
Humans
Imaging, Three-Dimensional
Mandibular Diseases - microbiology
Osteomyelitis - complications
Osteomyelitis - microbiology
Osteosclerosis - complications
Osteosclerosis - diagnostic imaging
Staphylococcal Infections - complications
Tomography, X-Ray Computed
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Summary:Dysosteosclerosis is a rare genetic disorder with a poor prognosis. It is an osteochondrodysplasia similar to osteopetrosis but it is typically characterized by platyspondyly and expanded metaphyses. It shows complications such as compression of cranial nerves, especially the optic nerve, hematologic complications, fractures following mild injury, abnormal dentition, neurological and psychological deterioration, in addition to osteomyelitis of the mandible. We report a new case of dysosteosclerosis complicated by osteomyelitis of the lower maxilla.
ISSN:1769-664X
DOI:10.1016/j.arcped.2015.08.005