Alveolar capillary dysplasia as a cause of persistent pulmonary hypertension

Background Persistent pulmonary hypertension (PPHN) in a term or late preterm has varied etiology. Case characteristics A late preterm neonate operated for esophageal atresia with tracheo-esophageal fistula was complicated by severe pulmonary hypertension and unable to be weaned off from respiratory...

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Bibliographic Details
Published in:Indian pediatrics 2015-11, Vol.52 (11), p.984-986
Main Authors: Razak, Abdul, Kumar Mohanty, Pankaj, Karthik Nagesh, N
Format: Article
Language:English
Subjects:
Case Report
Esophageal Atresia - etiology
Fatal Outcome
Humans
Infant, Newborn
Male
Maternal and Child Health
Medicine
Medicine & Public Health
Pediatric Surgery
Pediatrics
Persistent Fetal Circulation Syndrome - complications
Persistent Fetal Circulation Syndrome - diagnosis
Persistent Fetal Circulation Syndrome - physiopathology
Pulmonary Alveoli - abnormalities
Pulmonary Alveoli - physiopathology
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Summary:Background Persistent pulmonary hypertension (PPHN) in a term or late preterm has varied etiology. Case characteristics A late preterm neonate operated for esophageal atresia with tracheo-esophageal fistula was complicated by severe pulmonary hypertension and unable to be weaned off from respiratory support. Outcome The neonate expired by 15 weeks of life; diagnosis was made on postmortem lung biopsy. Message Alveolarcapillary dysplasia should be considered in a neonate with idiopathic refractory PPHN, if associated with anomalies.
ISSN:0019-6061
0974-7559
DOI:10.1007/s13312-015-0759-y