The Congenital Heart Surgeons’ Society Registry of Anomalous Aortic Origin of a Coronary Artery: an update

The anomalous aortic origin of a coronary artery from the wrong sinus of Valsalva with an interarterial, intramural, and/or intraconal course is a relatively rare congenital defect of the heart that may be associated with an increased risk of ischaemia of the myocardium and sudden death, notably in...

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Bibliographic Details
Published in:Cardiology in the young 2015-12, Vol.25 (8), p.1567-1571
Main Authors: Brothers, Julie A., Gaynor, J. William, Jacobs, Jeffrey P., Poynter, Jeffrey A., Jacobs, Marshall L.
Format: Article
Language:English
Subjects:
Adolescent
Adult
Angioplasty
Aorta, Thoracic - abnormalities
Cardiac arrhythmia
Cardiology
Child
Child, Preschool
Coronary Vessel Anomalies - complications
Coronary Vessel Anomalies - diagnosis
Coronary Vessel Anomalies - surgery
Death, Sudden, Cardiac - etiology
Female
Heart attacks
Humans
Infant
Infant, Newborn
Male
Original Articles
Registries
Societies, Medical
Thoracic Surgery
Veins & arteries
Young Adult
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Summary:The anomalous aortic origin of a coronary artery from the wrong sinus of Valsalva with an interarterial, intramural, and/or intraconal course is a relatively rare congenital defect of the heart that may be associated with an increased risk of ischaemia of the myocardium and sudden death, notably in children and young adults. Data are limited regarding stratification of risk and long-term outcomes of these patients. In 2009, the Anomalous Coronary Artery Working Group formed the Congenital Heart Surgeons’ Society Registry of Anomalous Aortic Origin of a Coronary Artery to obtain information on large numbers of young patients with anomalous aortic origin of a coronary artery with the goal to better understand the natural and surgical history of this anomaly as well as to develop evidence-based treatment and management guidelines. In this report, we describe the data we have collected from the registry and the current state of the registry.
ISSN:1047-9511
1467-1107
DOI:10.1017/S1047951115002061