Isolated left ventricular noncompaction causing refractory heart failure

Left ventricular noncompaction is a rare congenital anomaly characterized by excessive left ventricular trabeculation, deep intertrabecular recesses and a thin compacted layer due to the arrest of compaction of myocardial fibers during embryonic development. We report the case of a young patient wit...

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Bibliographic Details
Published in:Revista portuguesa de cardiologia 2016-03, Vol.35 (3), p.185.e1-185.e4
Main Authors: Meneguz-Moreno, Rafael Alexandre, Rodrigues da Costa Teixeira, Felipe, Rossi Neto, João Manoel, Finger, Marco Aurélio, Casadei, Carolina, Castillo, Maria Teresa, Sanchez de Almeida, Antonio Flávio
Format: Article
Language:Portuguese
Subjects:
Heart Defects, Congenital - complications
Heart Failure - etiology
Heart Transplantation - adverse effects
Heart Ventricles
Humans
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Summary:Left ventricular noncompaction is a rare congenital anomaly characterized by excessive left ventricular trabeculation, deep intertrabecular recesses and a thin compacted layer due to the arrest of compaction of myocardial fibers during embryonic development. We report the case of a young patient with isolated left ventricular noncompaction, leading to refractory heart failure that required extracorporeal membrane oxygenation followed by emergency heart transplantation.
ISSN:2174-2030
DOI:10.1016/j.repc.2015.09.015