Outcome of childhood-onset full-house nephropathy

Patients with full-house nephropathy (FHN) present renal lesions that are indistinguishable from those of lupus nephritis (LN) but lack the systemic features necessary to meet diagnostic criteria for systemic lupus erithematosus (SLE). Some have been reported to develop a delayed SLE with time. The...

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Bibliographic Details
Published in:Nephrology, dialysis, transplantation dialysis, transplantation, 2017-07, Vol.32 (7), p.1194-1204
Main Authors: Ruggiero, Barbara, Vivarelli, Marina, Gianviti, Alessandra, Pecoraro, Carmine, Peruzzi, Licia, Benetti, Elisa, Ventura, Giovanna, Pennesi, Marco, Murer, Luisa, Coppo, Rosanna, Emma, Francesco
Format: Article
Language:English
Subjects:
Adolescent
Age of Onset
Child
Disease Progression
Female
Glomerular Filtration Rate
Glomerulonephritis - diagnosis
Glomerulonephritis - etiology
Glomerulonephritis - mortality
Humans
Kidney Diseases - diagnosis
Kidney Diseases - etiology
Kidney Diseases - mortality
Lupus Erythematosus, Systemic - complications
Lupus Nephritis - diagnosis
Lupus Nephritis - etiology
Lupus Nephritis - mortality
Male
Proteinuria - pathology
Recurrence
Remission Induction
Retrospective Studies
Risk Factors
Survival Rate
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Summary:Patients with full-house nephropathy (FHN) present renal lesions that are indistinguishable from those of lupus nephritis (LN) but lack the systemic features necessary to meet diagnostic criteria for systemic lupus erithematosus (SLE). Some have been reported to develop a delayed SLE with time. The clinical outcome of children having FHN without SLE has never been reported. Children with biopsy-proven FHN were selected after excluding SLE cases by the absence of America College of Rheumatology criteria. The proportion of patients with complete (proteinuria
ISSN:0931-0509
1460-2385
DOI:10.1093/ndt/gfw230