Anomalous origin of the right coronary artery: First familial cases in Asia

Congenital coronary artery abnormalities may cause sudden death, particularly in athletes. Two siblings, aged 10 and 9 years, respectively, were diagnosed with anomalous origin of the right coronary artery on multi‐detector computed tomography (MDCT). The right coronary artery arose from the left co...

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Bibliographic Details
Published in:Pediatrics international 2016-11, Vol.58 (11), p.1232-1234
Main Authors: Motomura, Hideki, Yokokawa, Mari, Fukunaga, Hirofumi, Nakagaki, Mari, Hasuwa, Tomoyuki, Moriuchi, Hiroyuki
Format: Article
Language:English
Subjects:
abnormal origin
Angiography
Aorta
Asia
athlete
Athletes
Child
Computed tomography
Congenital diseases
Coronary Angiography - methods
Coronary artery
Coronary Vessel Anomalies - diagnosis
Coronary Vessel Anomalies - genetics
Coronary vessels
Coronary Vessels - diagnostic imaging
Diagnosis, Differential
EKG
Female
Genetic Predisposition to Disease
Heart
Humans
Ischemia
Male
Multidetector Computed Tomography
Pediatrics
Pulmonary arteries
Pulmonary artery
sibling
Siblings
sudden death
Tomography, X-Ray Computed
Ultrasonography
Ultrasound
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Summary:Congenital coronary artery abnormalities may cause sudden death, particularly in athletes. Two siblings, aged 10 and 9 years, respectively, were diagnosed with anomalous origin of the right coronary artery on multi‐detector computed tomography (MDCT). The right coronary artery arose from the left coronary cusp, and was wedged between the aorta and pulmonary artery. This was also noted on cardiac ultrasonography (UCG), but in general this might not be seen on electrocardiography at rest. Although the surgical indications are unclear in the case of unproven ischemia, early recognition of the condition may reduce risk of the cardiac events during exercise. The majority of proximal coronary artery anomalies can be screened for on UCG, and confirmed on MDCT, which yields more precise clinical details and is less invasive than angiography. This is the first report of familial cases of anomalous origin of the right coronary artery in Asia.
ISSN:1328-8067
1442-200X
DOI:10.1111/ped.13146