Ewing's sarcoma of the cranial vault: a case report

Ewing's sarcoma is a malignant tumor that mainly affects young patients. It represents 10% of primary malignant tumors of the bone and 3% of malignant tumors of the child. Cranial localization is extremely rare representing less than 1% of all the localizations. We report a case of a 10-year-ol...

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Bibliographic Details
Published in:Acta clinica belgica (English ed. Online) 2017-12, Vol.72 (6), p.443-446
Main Authors: Feki, Jihene, Guermazi, Zeineb, Kammoun, Brahim, Khanfir, Afef, Toumi, Nabil, Boudawara, Tahiya, Boudawara, Zaher, Daoud, Jamel, Frikha, Mounir
Format: Article
Language:English
Subjects:
Case reports
Chemotherapy
Child
Ewings sarcoma
Female
Humans
Parietal Bone
Sarcoma, Ewing - diagnosis
Sarcoma, Ewing - therapy
Skull Neoplasms - diagnosis
Skull Neoplasms - therapy
Tumors
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Summary:Ewing's sarcoma is a malignant tumor that mainly affects young patients. It represents 10% of primary malignant tumors of the bone and 3% of malignant tumors of the child. Cranial localization is extremely rare representing less than 1% of all the localizations. We report a case of a 10-year-old girl who presented with an intracranial hypertension syndrome with left parietal mass of progressive installation. The X-ray skull showed a lytic lesion with irregular margins involving the left parietal bone. Brain magnetic resonance imaging revealed extensive parietal bone destruction involving both the inner and outer tables. The girl was operated in emergency. Histological examination concluded to Ewing's Sarcoma. The resection was incomplete (R1). The girl received induction's chemotherapy. The cerebral scanner evaluation showed no abnormalities. Then, she received consolidation's chemotherapy with concomitant local radiation therapy. Currently, the girl is in complete remission with a seven-month decline.
ISSN:1784-3286
2295-3337
DOI:10.1080/17843286.2017.1300989