Retroperitoneal primitive neuroectodermal tumor (PNET): case report and review of literature

Primitive Neuroectodermal tumor belongs to the family of Ewing's tumor and is characterized by at (11;22) (q24;ql2) or at (21;22) (q22;ql2) translocation. Retroperitoneal primitive neuroectodermal tumor (PNET) are rare, usually affect young adults, and are often diagnosed late. There is no spec...

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Bibliographic Details
Published in:European journal of gynaecological oncology 2017, Vol.38 (2), p.314-318
Main Authors: Koch, A, Frigo, S, Lecointre, L, Hummel, M, Akladios, C Y, Bergerat, J P, Noël, G, Wattiez, A
Format: Article
Language:English
Online Access:Get full text
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Summary:Primitive Neuroectodermal tumor belongs to the family of Ewing's tumor and is characterized by at (11;22) (q24;ql2) or at (21;22) (q22;ql2) translocation. Retroperitoneal primitive neuroectodermal tumor (PNET) are rare, usually affect young adults, and are often diagnosed late. There is no specific characteristics for imaging. The diagnosis is made on histological examination of the surgical spec- imen or biopsies. Radiotherapy and chemotherapy complete the treatment. The authors report the case of a 26-year-old patient who only had pelvic discomfort. Diagnostic laparoscopy showed a retroperitoneal and retrovesical mass of five centimeters. The patient benefited from adjuvant chemotherapy and radiotherapy. She is free of disease 30 months after treatment.
ISSN:0392-2936
DOI:10.12892/ejgo3510.2017