Embryonal tumor with multilayered rosettes: illustrative case and review of the literature

Background Embryonal tumor with multilayered rosettes (ETMR) is a very rare entity and has seldom been reported. It has been newly defined tumor entity included in the latest update (revised fourth edition) of WHO 2016 Classification of Tumors of the Central Nervous System which portends a uniform d...

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Bibliographic Details
Published in:Child's nervous system 2018-12, Vol.34 (12), p.2361-2369
Main Authors: Bouali, Sofiene, Zehani, Alia, Mahmoud, Maha, Said, Imed Ben, Kallel, Jalel, Jemel, Hafedh
Format: Article
Language:English
Subjects:
Case-Based Update
Medicine
Medicine & Public Health
Neurosciences
Neurosurgery
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Summary:Background Embryonal tumor with multilayered rosettes (ETMR) is a very rare entity and has seldom been reported. It has been newly defined tumor entity included in the latest update (revised fourth edition) of WHO 2016 Classification of Tumors of the Central Nervous System which portends a uniform dismal prognosis and survival even with the best of multimodality approaches. Illustrative case This report documents the presentation of a 2-year-old girl with voluminous intracranial ETMR in the right parieto-occipital region. We describe clinical diagnosis, histological aspects, radiological features, and current management of this very aggressive tumor. Conclusion Pediatric intracranial ETMR is a highly aggressive neoplasm, and it should be considered in the differential diagnosis of pediatric brain tumors.
ISSN:0256-7040
1433-0350
DOI:10.1007/s00381-018-3972-x