Primary angiosarcoma of the femoral artery in patient with kidney and liver polycystosis and multiple arterial aneurysms: report of the case and review of the literature

The association between kidney and liver polycystosis and arterial aneurysms is well documented. However, it remains unclear whether these patients are at increased risk of malignant transformation. In this article, we describe a case of a primary angiosarcoma of the femoral artery with metastatic s...

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Bibliographic Details
Published in:Cardiovascular pathology 2019-03, Vol.39, p.8-11
Main Authors: Fabian, Ondrej, Mokra, Dana, Masopust, Jan, Skorepa, Jiri, Kodetova, Daniela Novakova, Zamecnik, Josef
Format: Article
Language:English
Subjects:
Aneurysm
Angiosarcoma
Femoral artery
Polycystic kidney
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Summary:The association between kidney and liver polycystosis and arterial aneurysms is well documented. However, it remains unclear whether these patients are at increased risk of malignant transformation. In this article, we describe a case of a primary angiosarcoma of the femoral artery with metastatic spread into the lungs and hilar lymph node arising in a 74-year-old man with kidney and liver polycystosis and multiple arterial aneurysms. •Primary intimal angiosarcoma is extremely rare.•A relationship between organ polycystosis and arterial aneurysms is well documented, but the association with angiosacroma is unclear.•There is no previous reference to angiosarcoma arising in this clinical setting.
ISSN:1054-8807
1879-1336
DOI:10.1016/j.carpath.2018.11.001