Absent Pulmonary Valve Syndrome in a Fetus: A Case Report and Literature Review

The main characteristics of absent pulmonary valve syndrome (APVS) include the absence or hypoplasia of the pulmonary valve, stenosis of the pulmonary valve annulus, and aneurysmal dilatation of the pulmonary trunk and its branches. In the more common type 1, the tetralogy of Fallot-like type, there...

Full description

Saved in:
Bibliographic Details
Published in:Fetal and pediatric pathology 2019-01, Vol.38 (1), p.57-62
Main Authors: Zhou, Wan-Ying, Li, Yue-Yi, He, Xiao-Qin, Wang, Yi-Bin
Format: Article
Language:English
Subjects:
Fetus - abnormalities
Heart Defects, Congenital - pathology
Humans
Male
Pulmonary Valve - abnormalities
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:The main characteristics of absent pulmonary valve syndrome (APVS) include the absence or hypoplasia of the pulmonary valve, stenosis of the pulmonary valve annulus, and aneurysmal dilatation of the pulmonary trunk and its branches. In the more common type 1, the tetralogy of Fallot-like type, there is a ventricular septal defect, overriding aorta, pulmonary arterial dilatation, and absence of ductus arteriosus, The second type has an intact ventricular septum, less pulmonary artery dilatation, and a patent ductus arteriosus, with or without tricuspid atresia. This APVS had an intact ventricular septum with an absent ductus arteriosus. The APVS with intact ventricular septum with an absent ductus arteriosus may represent a third type of APVS.
ISSN:1551-3815
1551-3823
DOI:10.1080/15513815.2018.1529066