Manifestation of congenital pulmonary airway malformation in a 26-year-old adult, requiring surgery

This is a case of type 1 congenital pulmonary airway malformation in the left lower lobe of a 26-year-old male. At the age of 1 year, he developed a pulmonary cystic lesion, which was considered to be bronchopulmonary sequestration. He grew up healthy and showed no impairment during exercise; howeve...

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Bibliographic Details
Published in:Interactive cardiovascular and thoracic surgery 2019-07, Vol.29 (1), p.154-156
Main Authors: Isowa, Masahide, Ueda, Satoshi, Sonobe, Makoto, Date, Hiroshi
Format: Article
Language:English
Subjects:
Adult
Cystic Adenomatoid Malformation of Lung, Congenital - diagnosis
Cystic Adenomatoid Malformation of Lung, Congenital - surgery
Humans
Lung - diagnostic imaging
Lung - surgery
Male
Pneumonectomy - methods
Tomography, X-Ray Computed
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Summary:This is a case of type 1 congenital pulmonary airway malformation in the left lower lobe of a 26-year-old male. At the age of 1 year, he developed a pulmonary cystic lesion, which was considered to be bronchopulmonary sequestration. He grew up healthy and showed no impairment during exercise; however, giant bullous lesion development along with compressed left upper lobe and mediastinum was recently noted; consequently, the patient was referred to our hospital for further examination. We diagnosed congenital pulmonary airway malformation and performed left lower lobectomy. Postoperative course was uneventful, but a restrictive change on pulmonary function test did not improve. This unusual course of congenital pulmonary airway malformation with bullous changes suggests the importance of early-stage resection.
ISSN:1569-9285
1569-9285
DOI:10.1093/icvts/ivz032