Individualized robotic organ‐sparing surgery in a paediatric case of renal perivascular epithelioid cell tumour

Background Perivascular epithelioid cell tumours (PEComas) represent a rare group of mesenchymal tumours with an unpredictable outcome. They are usually observed in middle‐aged women whilst they are very rare in children, with limited cases described. Due to the rare anatomical location in kidneys,...

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Bibliographic Details
Published in:The international journal of medical robotics + computer assisted surgery 2020-10, Vol.16 (5), p.1-4
Main Authors: Silveri, Massimiliano, Natali, Gian Luigi, Cobellis, Giovanni, Roberti, Agnese, Rossi, Sabrina, Gregori, Lorenzo, Torino, Giovanni
Format: Article
Language:English
Subjects:
Children
Kidneys
metanephric stromal tumour
Neoplasms
partial nephrectomy
Pediatrics
rare tumours
renal tumours
robotic
Robotic surgery
Tumors
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Summary:Background Perivascular epithelioid cell tumours (PEComas) represent a rare group of mesenchymal tumours with an unpredictable outcome. They are usually observed in middle‐aged women whilst they are very rare in children, with limited cases described. Due to the rare anatomical location in kidneys, a correct diagnosis and treatment is really challenging. Methods We observed and treated a case of kidney's PEComa in a 14‐year‐old boy. Results An individualized approach based on anatomical (3D CT‐reconstructions) and histopathological (US‐guided preliminary biopsy) features lead us to perform a successful robotic‐sparing surgery enabling the preservation of two‐thirds of the kidney involved. Conclusions A meticulous preoperative planning in selected patients can lead to a minimally invasive approach even in some paediatric kidney's neoplasms.
ISSN:1478-5951
1478-596X
DOI:10.1002/rcs.2142