Fragile X syndrome in young females: Influence of executive function on the neurocognitive profile and adaptive behavior

The aim of this study is to describe the relationship between executive function (EF) and performance in different areas of the neurocognitive profile in young girls with Fragile-X-Syndrome (FXS). A neuropsychological assessment was carried out to 40 female participants aged 7–16 years (26 FXS, 14 c...

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Bibliographic Details
Published in:Research in developmental disabilities 2021-05, Vol.112, p.103912-103912, Article 103912
Main Authors: Joga-Elvira, Lorena, Jacas, Carlos, Joga, María Luisa, Roche-Martínez, Ana, Brun-Gasca, Carme
Format: Article
Language:English
Subjects:
Adaptive behavior
Executive function
Females
Fragile-X-Syndrome
Neurocognitive profile
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Summary:The aim of this study is to describe the relationship between executive function (EF) and performance in different areas of the neurocognitive profile in young girls with Fragile-X-Syndrome (FXS). A neuropsychological assessment was carried out to 40 female participants aged 7–16 years (26 FXS, 14 control group). Regarding intellectual ability, in the group of girls with FXS 3.84 % of the participants obtained IQ scores in the range of moderate ID (IQ 35–40 to 49), 46.15 % in the range of mild ID (IQ 50–70), 38.46 % in the borderline range (IQ 70–85), and 11.53 % within the average range (IQ > 85). EF was found to have a greater influence on adaptive behavior, arithmetic ability, theory of mind, leadership, social integration, social competence, and anxiety/shyness in the group with FXS. In girls with FXS, EF showed a greater influence on adaptive behavior, arithmetic ability, and social domain.
ISSN:0891-4222
1873-3379
DOI:10.1016/j.ridd.2021.103912