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Clinical management of amyloid cardiomyopathy
Clinical heart failure, restrictive cardiomyopathy, and arrhythmias are hallmark features of amyloid cardiomyopathy. In contrast to the advancements in targeted therapies, there is a general lack of evidence-based practice guidelines for clinical management of amyloid cardiomyopathy. In this review,...
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Published in: | Heart failure reviews 2022-09, Vol.27 (5), p.1549-1557 |
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container_title | Heart failure reviews |
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creator | Kim, Morris M. Kolseth, Clinton M. Carlson, Dayna Masri, Ahmad |
description | Clinical heart failure, restrictive cardiomyopathy, and arrhythmias are hallmark features of amyloid cardiomyopathy. In contrast to the advancements in targeted therapies, there is a general lack of evidence-based practice guidelines for clinical management of amyloid cardiomyopathy. In this review, we review the role of routine medical therapy in amyloid cardiomyopathy, from heart failure management to orthostatic hypotension, atrial arrhythmias, thromboembolic complications, and prevention of sudden death. We conclude by discussing approaches to patients with end-stage disease. |
doi_str_mv | 10.1007/s10741-021-10159-w |
format | article |
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subjects | Amyloid Amyloidosis Beta blockers Cardiac arrhythmia Cardiology Cardiomyopathy Congestive heart failure Diuretics Drug dosages Enzymes Heart failure Hemodynamics Hospitalization Hypertension Hypotension Medicine Medicine & Public Health Orthostatic hypotension Pulmonary arteries Stroke Thromboembolism |
title | Clinical management of amyloid cardiomyopathy |
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