A case of tricuspid atresia with pulmonary valve absence coexisting coronary-right ventricular fistula

Tricuspid atresia with pulmonary valve absence is a rare malformation characterized by left ventricular outflow obstruction due to asymmetrical ventricular septal hypertrophy and associated with a poor prognosis. Coexisting coronary-right ventricular fistula is rarely described. We encountered a cas...

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Bibliographic Details
Published in:General thoracic and cardiovascular surgery 2021-12, Vol.69 (12), p.1585-1588
Main Authors: Fujita, Satoshi, Tatewaki, Hideki, Nagatomo, Yusaku, Shiose, Akira
Format: Article
Language:English
Subjects:
Anticoagulants
Cardiac Surgery
Cardiology
Case Report
Catheters
Coronary vessels
Fistula
Heart
Medicine
Medicine & Public Health
Pulmonary arteries
Surgical Oncology
Sutures
Thoracic Surgery
Veins & arteries
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Summary:Tricuspid atresia with pulmonary valve absence is a rare malformation characterized by left ventricular outflow obstruction due to asymmetrical ventricular septal hypertrophy and associated with a poor prognosis. Coexisting coronary-right ventricular fistula is rarely described. We encountered a case of tricuspid atresia with pulmonary valve absence coexisting coronary-right ventricle fistula that successfully underwent Fontan completion. Right ventricle dilatation due to coronary-right ventricle fistula was observed in addition to mass like ventricular septal hypertrophy protruding into the left ventricular outflow tract. Right ventricle reduction and prevention of progressive left ventricular outflow obstruction were achieved by closure of the coronary-right ventricle fistula closure and plication of the right ventricle with the bidirectional Glenn procedure.
ISSN:1863-6705
1863-6713
DOI:10.1007/s11748-021-01702-5