Histopathological characteristics of the arrhythmogenic right ventricular cardiomyopathy presenting the electrocardiographic characteristics with Brugada syndrome

The histopathological characteristics of the overlapping disease states of Brugada syndrome (BrS) and arrhythmogenic right ventricular cardiomyopathy (ARVC) have not been fully elucidated. A 71-year-old man showed coved-type ST-segment elevation with the right precordial leads, and the echocardiogra...

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Bibliographic Details
Published in:Journal of cardiovascular electrophysiology 2023-09, Vol.34 (9), p.2006-2009
Main Authors: Murase, Yosuke, Igawa, Osamu, Imai, Hajime, Ogawa, Yasuhiro, Kano, Naoaki, Mamiya, Keita, Ikeda, Tomoyo, Miyamae, Kiichi, Yamazoe, Shinji, Torii, Jun, Yamanaka, Kazuyuki, Kato, Toshimasa, Kawaguchi, Kenta, Kawaguchi, Katsuhiro
Format: Article
Language:English
Subjects:
Autopsy
Cardiomyopathy
Echocardiography
Ventricle
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Summary:The histopathological characteristics of the overlapping disease states of Brugada syndrome (BrS) and arrhythmogenic right ventricular cardiomyopathy (ARVC) have not been fully elucidated. A 71-year-old man showed coved-type ST-segment elevation with the right precordial leads, and the echocardiography demonstrated right ventricular (RV) dilatation. After 11 months, he died of a polymorphic VT storm. The pathological tissue demonstrated fibrofatty degeneration in the free wall of the RV outflow tract based on the heart autopsy. The overlapping disease states of BrS and ARVC showed histopathological characteristics consistent with ARVC.
ISSN:1045-3873
1540-8167
1540-8167
DOI:10.1111/jce.16037