Systemic under treatment of heart disease in patients with Duchenne muscular dystrophy

•Two-thirds of Duchenne muscular dystrophy patients are not receiving the recommended prophylactic cardiac treatment.•Since the recommendation of prophylactic cardiac care for Duchenne muscular dystrophy was published those patients receiving cardiac directed therapies initiated that care significan...

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Bibliographic Details
Published in:Neuromuscular disorders : NMD 2023-10, Vol.33 (10), p.776-781
Main Authors: Karachunski, Peter, Townsend, DeWayne
Format: Article
Language:English
Subjects:
clinical management
Duchenne muscular dystrophy
dystrophic cardiomyopathy
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Summary:•Two-thirds of Duchenne muscular dystrophy patients are not receiving the recommended prophylactic cardiac treatment.•Since the recommendation of prophylactic cardiac care for Duchenne muscular dystrophy was published those patients receiving cardiac directed therapies initiated that care significantly sooner.•Implementation of early cardiac directed therapies represent an important opportunity to improve the management of cardiac disease in patients with Duchenne muscular dystrophy. Duchenne muscular dystrophy is a devastating muscle disease characterized by muscle deterioration and cardiomyopathy. The cardiomyopathy is progressive in nature, marked by the accumulation of myocardial scarring and the loss of contractile function. The presence of cardiac disfunction is nearly universal in individuals with Duchenne muscular dystrophy with dysfunction being evident in patients
ISSN:0960-8966
1873-2364
DOI:10.1016/j.nmd.2023.09.004