Anesthetic Management of a Patient With Spinocerebellar Ataxia Type 1

Spinocerebellar ataxia type 1 (SCA1) is one of the autosomal dominant spinocerebellar degeneration (SCD) diseases characterized by progressive cerebellar ataxia, muscle atrophy, and peripheral neuropathy. We report the management of a 43-year-old man with SCA1 who underwent general anesthesia for op...

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Bibliographic Details
Published in:Anesthesia progress 2023-12, Vol.70 (4), p.194-195
Main Authors: Takeda, Sakura, Idzuchi, Sumire, Mizuta, Kentaro
Format: Article
Language:English
Subjects:
Airway management
Analgesics
Anesthesia
Anesthesiology
Ataxia
Ataxin
Atrophy
Cerebellar ataxia
Cerebellum
Dentistry
Dysphagia
Fentanyl
General anesthesia
Hypotension
Intubation
Laryngoscopy
Narcotics
Paralysis
Patients
Peripheral neuropathy
Spinocerebellar ataxia
Surgery
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Summary:Spinocerebellar ataxia type 1 (SCA1) is one of the autosomal dominant spinocerebellar degeneration (SCD) diseases characterized by progressive cerebellar ataxia, muscle atrophy, and peripheral neuropathy. We report the management of a 43-year-old man with SCA1 who underwent general anesthesia for open reduction and internal fixation of a mandibular fracture. Although anesthesia-induced vocal cord paralysis has been reported in patients with SCD, nasotracheal intubation was performed uneventfully with video laryngoscope. After taking into consideration the increased risk of postoperative respiratory depression in patients with SCD, rocuronium dosing was titrated carefully, and fentanyl was not used during surgery. Preparation for an anticipated difficult airway and avoiding significant respiratory depression are crucial when providing general anesthesia for patients with SCA1.
ISSN:0003-3006
1878-7177
DOI:10.2344/anpr-70-03-05