Right Ventricular and Outflow Tract Functional Characteristics After Repair of Tetralogy of Fallot with Major Aortopulmonary Collaterals

• Published in: Pediatric cardiology 2024-04, Vol.45 (4), p.795-803
• Main Authors: Long, Zsofia B., Punn, Rajesh, Zhang, Yulin, Arunamata, Alisa A., Asija, Ritu, Ma, Michael, Hanley, Frank L., McElhinney, Doff B.
• Format: Article
• Language: English
• Subjects: Cardiac Surgery; Cardiac Surgical Procedures; Cardiology; Heart Failure; Heart Ventricles; Humans; Medicine; Medicine & Public Health; Pulmonary Valve Stenosis - surgery; Retrospective Studies; Tetralogy of Fallot - diagnostic imaging; Tetralogy of Fallot - surgery; Vascular Surgery; Ventricular Function, Right
• ISSN: 0172-0643; 1432-1971
• DOI: 10.1007/s00246-024-03412-0

This study describes right ventricle (RV) characteristics and right ventricle to pulmonary artery (RV-PA) conduit function pre- and post-repair in patients with tetraology of Fallot with major aortopulmonary collaterals (TOF/MAPCAs). We reviewed patients who underwent single-stage, complete unifocalization, and repair of TOF/MAPCAs between 2006 and 2019 with available pre- and early postoperative echocardiograms. For a subset of patients, 6–12 month follow-up echocardiogram was available. RV and left ventricle (LV) characteristics and RV-PA conduit function were reviewed. Wilcoxon signed rank test and McNemar’s test were used. 170 patients were reviewed, 46 had follow-up echocardiograms. Tricuspid valve annular plane systolic excursion (TAPSE) Z-scores were reduced from pre- (Z-score 0.01) to post-repair (Z-score −4.5, p