Aortopathy and aortic valve surgery in patients with bicuspid aortic valve with and without raphe

• Published in: International journal of cardiology 2024-07, Vol.407, p.132000-132000, Article 132000
• Main Authors: Bellino, Michele, Antonini-Canterin, Francesco, Bossone, Eduardo, Faggiano, Pompilio, Chirillo, Fabio, La Carrubba, Salvatore, Faganello, Giorgio, Cecconi, Moreno, Zito, Concetta, Dasseni, Nicolò, Nistri, Stefano, Moreo, Antonella, Fabiani, Iacopo, Faden, Giacomo, Agostini, Francesco, Manuppelli, Vincenzo, Cameli, Matteo, Cresti, Alberto, Dentamaro, Ilaria, Monte, Ines Paola, Barbieri, Andrea, Ciampi, Quirino, Giorgi, Mauro, Galasso, Gennaro, Carerj, Scipione, Pepi, Mauro, Benedetto, Frank, Colonna, Paolo, Citro, Rodolfo
• Format: Article
• Language: English
• Subjects: Adult; Aged; Aortic Diseases - diagnostic imaging; Aortic Diseases - epidemiology; Aortic Diseases - surgery; Aortic Valve - abnormalities; Aortic Valve - diagnostic imaging; Aortic Valve - surgery; Aortic Valve Stenosis - diagnostic imaging; Aortic Valve Stenosis - surgery; Aortopathy; Bicuspid aortic valve; Bicuspid Aortic Valve Disease - complications; Bicuspid Aortic Valve Disease - diagnostic imaging; Bicuspid Aortic Valve Disease - surgery; Female; Follow-Up Studies; Heart Valve Diseases - complications; Heart Valve Diseases - diagnostic imaging; Heart Valve Diseases - surgery; Humans; Italy - epidemiology; Male; Middle Aged; Registries; Valvulopathy
• ISSN: 0167-5273; 1874-1754
• DOI: 10.1016/j.ijcard.2024.132000

To evaluate the association between raphe in bicuspid aortic valve (BAV) patients and valve dysfunction, aortopathy and aortic valve surgery in the REBECCA registry [REgistro della valvola aortica Bicuspide della Società Italiana di ECocardiografia e CArdiovascular Imaging (SIECVI)]. Prevalence of aortic valve dysfunction and aortopathy was investigated in BAV patients with and without raphe. Aortic valve dysfunction (regurgitation or stenosis) was categorized as mild, moderate and severe. Aortopathy was defined as annulus ≥14 mm/m2; root ≥20 mm/m2; sinotubular junction ≥16 mm/m2; ascending aorta ≥17 mm/m2, and classified in Type A, isolated ascending aorta dilatation; Type B, aortic root and ascending aorta dilatation; and Type C, isolated aortic root dilatation. Overall, 695 patients with BAV were enrolled; 520 (74.8%) with raphe and 175 (25.2%) without raphe. BAV patients with raphe presented more frequently with moderate or severe aortic stenosis than BAV patients without raphe (183 [35.2%] vs 34 [19.4%], p